Mortality in sickle cell disease. Life expectancy and risk factors for early death.
Explore this paper's citation graph
Summary
Modeling revealed that in patients with sickle cell anemia, the acute chest syndrome, renal failure, seizures, a base-line white-cell count above 15,000 cells per cubic millimeter, and a low level of fetal hemoglobin were associated with an increased risk of early death.
- Type
- article
- Published
- 1994-06-09
- Cited by
- 3,328
- References
- 17
- Access
- Open access
- OpenAlex
- https://openalex.org/W2334263927
- Semantic Scholar
- https://api.semanticscholar.org/CorpusID:36677849
Keywords
Medicine, Sickle cell anemia, Life expectancy, Disease, Thalassemia
References
- Is pain crisis a cause of death in sickle cell disease?
- White blood cell count as a predictor of mortality: results over 18 years from the Normative Aging Study.
- The variable expression of sickle cell disease is genetically determined.
- Effects of thalassemia and microcytosis on the hematologic and vasoocclusive severity of sickle cell anemia.
- α-Globin gene organisation in blacks precludes the severe form of α-thalassaemia
- Mortality in children and adolescents with sickle cell disease. Cooperative Study of Sickle Cell Disease.
- Infarction of bone marrow in the sickle cell disorders.
- Intravenous narcotic therapy for children with severe sickle cell pain crisis.
- Survival analysis in natural history studies of disease.
- The lung in sickle cell disease.
- Causes of death in sickle-cell disease in Jamaica.
- The Haemolytic Anaemias: Congenital and Acquired
- Two different molecular organizations account for the single alpha-globin gene of the alpha-thalassemia-2 genotype.
- Stability over time of hematological variables in 197 children with sickle cell anemia.
- Fat embolism in sickle cell disease
- Pain in sickle cell disease. Rates and risk factors.
- The cooperative study of sickle cell disease: review of study design and objectives.
- Fat embolism in sickle cell disease. Report of a case with brief review of the literature
Cited by
- Knowledge of Sickle Cell Trait and Disease among African-American College Students
- Sickle Cell Disease Screening Programs
- The Effects of Family Functioning on Academic Achievement in Children with Sickle Cell Disease
- Direct surface sampling of dried blood spots coupled with mass spectrometry for haemoglobin analysis
- Effects of a long-term transfusion regimen on sickle cell-related illnesses.
- Sickle cell disease: implications for perioperative care.
- Screening for sickle cell disease and thalassaemia: a systematic review with supplementary research.
- Early onset dactylitis associated with the occurrence of severe events in children with sickle cell anaemia. The Paediatric Cohort of Guadeloupe (1984-99).
- The epidemiology of stroke in sickle cell patients in Yaounde, Cameroon.
- Impact of proximity to comprehensive sickle cell center on utilization of healthcare services among children with sickle cell disease
- 51Cr-EDTA measurements of the glomerular filtration rate in patients with sickle cell anaemia and minor renal damage
- Patient‐controlled analgesia versus continuous infusion of morphine during vaso‐occlusive crisis in sickle cell disease, a randomized controlled trial
- Microvascular endothelial cells express a phosphatidylserine receptor: a functionally active receptor for phosphatidylserine-positive erythrocytes.
- Characteristics and outcome of connective tissue diseases in patients with sickle-cell disease: report of 30 cases.
- DNA polymorphisms at the BCL11A, HBS1L-MYB, and β-globin loci associate with fetal hemoglobin levels and pain crises in sickle cell disease
- A primary care provider's guide to preventive and acute care management of adults and children with sickle cell disease
- Novel therapies in sickle cell disease.
- Sickle cell disease: new insights into pathophysiology and treatment.
- Endothelin in renal injury due to sickle cell disease.
- Sickle cell nephropathy – a practical approach
Related papers
- Molecular characterization of thalassemia and hemoglobinopathy in Southeastern China
- Recent progress in laboratory diagnosis of thalassemia and hemoglobinopathy: a study by the Korean Red Blood Cell Disorder Working Party of the Korean Society of Hematology
- Diagnostic strategy for thalassemias and other hemoglobinopathies: a program applied to the Hellenic Army recruits.
- Thalassemias and Hemoglobinopathies in Turkey
- Kelainan pada Sintesis Hemoglobin: Thalassemia dan Epidemiologi Thalassemia
- Sickle cell anemia, sickle cell β-thalassemia, and thalassemia major in Albania: characterization of mutations
- Thalassemia
- [Insufficient urine concentration in sickle cell anemia and S-C hemoglobinopathy. Study of 56 patients].