A surfactant protein C precursor protein BRICHOS domain mutation causes endoplasmic reticulum stress, proteasome dysfunction, and caspase 3 activation.

Keywords

Unfolded protein response, Endoplasmic reticulum, Surfactant protein C, Cell biology, Proteasome

References

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Cited by

• Defects in surfactant synthesis: clinical implications.Lourdes Ayxendri — 2006
• A novel surfactant protein C L55F mutation associated with interstitial lung disease alters subcellular localization of proSP-C in A549 cellsPatrick Jamieson, Binod Rizal, Svet Simidjiyski — 2016
• Proteostasis in pediatric pulmonary pathologyAna Cláudia Gruszynski, Cida Golin — 2014
• MiR-199a-5p, un « fibromiR » amplificateur de la voie du TGF-beta dans la fibrose pulmonaire idiopathiqueImène-Sarah Henaoui — 2013
• Regulation of the Proteasome: Evaluating the Lung Proteasome as a New Therapeutic TargetSilke Meiners, Ilona E. Keller, Nora Semren — 2014
• Synthetic pulmonary surfactant : Effects of surfactant proteins B and C and their analoguesAndreas Almlén — 2010
• Protein misfolding and amyloid formationCharlotte Nerelius — 2009
• Interstitial Lung Disease in Childhood: Clinical and Genetic AspectsHiroshi Kitazawa, Shigeo Kure — 2015
• Linking progression of fibrotic lung remodeling and ultrastructural alterations of alveolar epithelial type II cells in the amiodarone mouse model.Bastian Birkelbach, Dennis Lutz, Clemens Ruppert — 2015
• Zellbiologische Charakterisierung von Surfactant Protein C Mutationen bei Interstitiellen LungenkrankheitenT. Thurm — 2014
• The Genetic Approach in Pulmonary FibrosisWilliam E. Lawson, James E. Loyd — 2012
• C‐terminal, endoplasmic reticulum‐lumenal domain of prosurfactant protein C – structural features and membrane interactionsCristina Casals, Hanna Johansson, A. Sáenz — 2008
• Pathogenesis of idiopathic pulmonary fibrosis: review of recent findingsElisabetta Renzoni, Srihari Veeraraghavan, Piersante Sestini — 2014
• The three R's of lung health and disease: repair, remodeling, and regeneration.Michael F. Beers, Edward E. Morrisey — 2011
• Protein C Mutation (A267T) Results in ER Retention and Unfolded Protein Response ActivationLena Tjeldhorn, Nina Iversen, Kirsten Sandvig — 2011
• Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection.William E. Lawson, Peter F. Crossno, Vasiliy V. Polosukhin — 2008
• The surfactant protein C mutation A116D alters cellular processing, stress tolerance, surfactant lipid composition, and immune cell activationRalf Zarbock, Markus Woischnik, Christiane Sparr — 2012
• Idiopathic Pulmonary FibrosisJessica Adkins, Harold R. Collard — 2019
• Fibrosis of Two: Epithelial Cell-Fibroblast Interactions in Pulmonary FibrosisNorihiko Sakai, Andrew M. Tager — 2013
• Clinical and ultrastructural spectrum of diffuse lung disease associated with surfactant protein C mutationsDonatella Peca, Renata Boldrini, Jan Johannson — 2015

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