Pulmonary arterial hypertension in congenital heart disease: an epidemiologic perspective from a Dutch registry.
Explore this paper's citation graph
Summary
PAH is common in adult patients with congenital heart disease and in the authors' registry the prevalence of PAH in septal defects is around 6%.
- Type
- article
- Published
- 2007-08-21
- Cited by
- 354
- References
- 23
- OpenAlex
- https://openalex.org/W1987388573
- Semantic Scholar
- https://api.semanticscholar.org/CorpusID:31797073
Keywords
Medicine, Heart disease, Pulmonary hypertension, Eisenmenger syndrome, Internal medicine
References
- Incidence of secondary pulmonary hypertension in adults with atrial septal or sinus venosus defects
- Pulmonary hypertension after operations for congenital heart disease: analysis of risk factors and management.
- Clinical Correlates and Reference Intervals for Pulmonary Artery Systolic Pressure Among Echocardiographically Normal Subjects
- Diagnosis and differential assessment of pulmonary arterial hypertension.
- The Eisenmenger Syndrome
- The Eisenmenger Syndrome in Adults
- Hipertensión arterial pulmonar en adultos con cardiopatía congénita
- Evaluation and Management of the Patient with Pulmonary Arterial Hypertension
- Prognosis for patients with Eisenmenger syndrome of various aetiology.
- Prognosis of pulmonary arterial hypertension: ACCP evidence-based clinical practice guidelines.
- BMPR2 mutations in pulmonary arterial hypertension with congenital heart disease
- Isolated atrial septal defect with pulmonary vascular obstructive disease--long-term follow-up and prediction of outcome after surgical correction.
- Adherence to guidelines in the clinical care for adults with congenital heart disease: the Euro Heart Survey on adult congenital heart disease.
- The spectrum of adult congenital heart disease in Europe: morbidity and mortality in a 5 year follow-up period. The Euro Heart Survey on adult congenital heart disease.
- Pulmonary arterial hypertension in congenital heart disease.
- Eisenmenger syndrome. Factors relating to deterioration and death.
- Possibilities and impossibilities in the evaluation of pulmonary vascular disease in congenital heart defects.
- Natural history of atrial septal defect.
- Exercise Intolerance in Adult Congenital Heart Disease: Comparative Severity, Correlates, and Prognostic Implication
- CONCOR, An Initiative towards a National Registry and DNA-bank of Patients with Congenital Heart Disease in the Netherlands: Rationale, Design, and Frst Results
Cited by
- Pulmonary Arterial Hypertension Associated with Congenital Heart Disease and Eisenmenger Syndrome: Current Practice in Pediatrics
- Diagnosis of pulmonary hypertension in the congenital heart disease adult population impact on outcomes.
- 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: Executive Summary: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines.
- Pulmonale Hypertonie und pulmonale Zirkulation bei angeborenen Herzfehlern
- Smooth muscle cell proliferation and endothelin pathway in pulmonary arterial hypertension : comparative effects of current and putative therapeutic agents
- No inflammatory response related to pulmonary hemodynamics in children with systemic to pulmonary shunts.
- Can "inoperable" congenital heart defects become operable in patients with pulmonary arterial hypertension? Dream or reality?
- Syndrome d’Eisenmenger
- A binational registry of adults with pulmonary arterial hypertension complicating congenital heart disease
- Life span of patients with Eisenmenger syndrome is not superior to that of patients with other causes of pulmonary hypertension.
- Pulmonary Hypertension in Congenital Heart Disease: Beyond Eisenmenger Syndrome.
- Interventions for treating pulmonary hypertension in people with sickle cell disease or thalassaemia
- Facing the future of adults with congenital heart disease
- Congenital heart disease‐associated pulmonary arterial hypertension: preliminary results from a novel registry
- Right Ventricular Function in Adult Patients with Eisenmenger Physiology: Insights from Quantitative Echocardiography
- Pulmonary arterial hypertension in adults with congenital heart disease
- Adult Congenital Heart Disease and Pulmonary Arterial Hypertension: The Texas Adult Congenital Heart Program Experience
- The Belgian Eisenmenger syndrome registry: Implications for treatment strategies?
- Efficacy of exercise training in pulmonary arterial hypertension associated with congenital heart disease.
- The changing epidemiology of congenital heart disease
Related papers
- Chronic α1 blockade in a patient with Eisenmenger syndromeblockade in a patient with Eisenmenger syndrome
- Defining heart failure in adult congenital heart disease
- PAH-Associated Congenital Heart Disease: Finding Common Ground With Primary Pulmonary Hypertension
- Pulmonary Hypertension in Congenital Heart Disease: Beyond Eisenmenger Syndrome.
- Postoperative care of 13 cases with congenital heart disease with pulmonary hypertension
- Pulmonary Arterial Hypertension in Congenital Heart Diseases
- [Congenital cardiopathies in adults].
- Operative treatment of ventricular septal defect complicated by "critical" pulmonary hypertension
- Natural histories of atrial septal defect with pulmonary hypertension, and ventricular septal defect with pulmonary hypertension.
- Unidirectional Valved Patch Closure of Ventricular Septal Defect with Eisenmenger Physiology